Tracheobronchomegaly | |
---|---|
Other names | Mounier-Kühn syndrome [1] |
Specialty | Pulmonology |
Complications | Recurrent pulmonary infections |
Causes | atrophy of elastic fibers in the trachea and main bronchi, leading to thinning of the smooth muscle layer |
Diagnostic method | CT Chest. Tracheobroncheal flaccidity, dilatation, and/or collapse. |
Frequency | 300 cases have been reported to date |
Tracheobronchomegaly is a very rare congenital disorder of the lung primarily characterized by an abnormal widening of the upper airways. [2] The abnormally widened trachea and mainstem bronchi are associated with recurrent lower respiratory tract infection and copious purulent sputum production, eventually leading to bronchiectasis and other respiratory complications. [3]
Woodring et al. (1991) suggested the following diagnostic criteria for tracheomegaly in adults based on chest radiography: [4]
The term "Mounier-Kuhn syndrome" derives from the characterization of the condition by Prof. Pierre-Louis Mounier-Kuhn in 1932, while the name "tracheobronchomegaly" was introduced by Katz et al. in 1962. [5] [6] [7]
{{
cite web}}
: CS1 maint: numeric names: authors list (
link)
Tracheobronchomegaly | |
---|---|
Other names | Mounier-Kühn syndrome [1] |
Specialty | Pulmonology |
Complications | Recurrent pulmonary infections |
Causes | atrophy of elastic fibers in the trachea and main bronchi, leading to thinning of the smooth muscle layer |
Diagnostic method | CT Chest. Tracheobroncheal flaccidity, dilatation, and/or collapse. |
Frequency | 300 cases have been reported to date |
Tracheobronchomegaly is a very rare congenital disorder of the lung primarily characterized by an abnormal widening of the upper airways. [2] The abnormally widened trachea and mainstem bronchi are associated with recurrent lower respiratory tract infection and copious purulent sputum production, eventually leading to bronchiectasis and other respiratory complications. [3]
Woodring et al. (1991) suggested the following diagnostic criteria for tracheomegaly in adults based on chest radiography: [4]
The term "Mounier-Kuhn syndrome" derives from the characterization of the condition by Prof. Pierre-Louis Mounier-Kuhn in 1932, while the name "tracheobronchomegaly" was introduced by Katz et al. in 1962. [5] [6] [7]
{{
cite web}}
: CS1 maint: numeric names: authors list (
link)